L-Carnitine hydrochloride is a highly polar small zwitterion and is an important cofactor for the mitochondrial β-oxidation pathway. L-Carnitine hydrochloride is used to transport long-chain fat acyl coA into mitochondria for β-oxidative degradation. L-Carnitine hydrochloride is used as an antioxidant. L-Carnitine hydrochloride is used to improve metabolic imbalances for many inborn errors of metabolism.